KMID : 0980720150340020204
|
|
Keimyung Medical Journal 2015 Volume.34 No. 2 p.204 ~ p.208
|
|
A Case of Hepatic Involvement in Hereditary Hemorrhagic Telangiectasia Presenting as High Output Heart Failure
|
|
¹ÎÁؽÄ:Min Jun-Sik
¹ÚÇü¿:Park Hyoung-Yoel/¹ÚÁ¾ÀÍ:Park Jong-Ik/¹Ú¼¼·É:Park Se-Ryeong/Á¦°¥¹®:Jaegal Moon/À̼ººó:Lee Seong-Byn
|
|
Abstract
|
|
|
Hereditary hemorrhagic telangiectasia (HHT), also known as Osler-Weber-Rendu disease, is a rare autosomal dominant vascular disorder involving arteriovenous malformation. HHT is characterized by recurrent epistaxis, cutaneous telangiectasia, and visceral arteriovenous malformations. Hepatic arteriovenous malformation can lead to high output heart failure. We report a case of hereditary hemorrhagic telangiectasia patient who complained dyspnea and edema on both lower extremity.
|
|
KEYWORD
|
|
Arteriovenous malformation, Heart failure, Hereditary hemorrhagic telangiectasia
|
|
FullTexts / Linksout information
|
|
|
|
Listed journal information
|
|
|